A histologic study of nonmorphogenetic forms of hereditary hearing impairment

RJH Smith, KP Steel, C Barkway… - … –Head & Neck …, 1992 - jamanetwork.com
• It appears that many forms of syndromic and nonsyndromic hereditary hearing impairment
are secondary to either neuroepithelial or cochleosaccular dysfunction. Making this
distinction can be difficult in human temporal bone specimens; however, this added
knowledge may ultimately provide prognostic and therapeutic information in hearing
habilitation. Fundamental studies using animal models of different types of hereditary
deafness may also prove useful in this respect.(Arch Otolaryngol Head Neck Surg. 1992; …