Klippel-Trénaunay syndrome: the importance of “geographic stains” in identifying lymphatic disease and risk of complications
C Maari, IJ Frieden - Journal of the American Academy of Dermatology, 2004 - Elsevier
BACKGROUND: Klippel-Trénaunay syndrome (KTS) is a rare congenital anomaly
classically defined as the triad of vascular stain, soft tissue and/or bony hypertrophy, and
venous varicosities. OBJECTIVE: To determine whether the morphologic characteristics of
the associated vascular stains in KTS are predictive of the presence of lymphatic
involvement and/or complications. SETTING: Outpatient dermatology practice, tertiary care
medical center. METHODS: We retrospectively reviewed all cases of KTS identified between …
classically defined as the triad of vascular stain, soft tissue and/or bony hypertrophy, and
venous varicosities. OBJECTIVE: To determine whether the morphologic characteristics of
the associated vascular stains in KTS are predictive of the presence of lymphatic
involvement and/or complications. SETTING: Outpatient dermatology practice, tertiary care
medical center. METHODS: We retrospectively reviewed all cases of KTS identified between …
