Lymphangioleiomyomatosis and tuberous sclerosis complex in Quebec: prevalence and health-care utilization

AS Kristof, PZ Li, P Major, JS Landry - Chest, 2015 - Elsevier
BACKGROUND Lymphangioleiomyomatosis (LAM) is a manifestation of tuberous sclerosis
complex (TSC) that causes destruction of the lung and chronic respiratory failure. Population-
based estimates of demographics, clinical outcomes, and health-care utilization are lacking
for TSC and LAM. METHODS Data on demographics, clinical outcomes, and health-care
utilization in the Quebec ministerial provincial health-care database were analyzed for their
association with TSC and LAM. RESULTS A total of 1,004 subjects with TSC were identified …