[HTML][HTML] Stone man: a case report

H Mortazavi, M Eshghpour, M Niknami… - Iranian Journal of …, 2013 - ncbi.nlm.nih.gov
Iranian Journal of Radiology, 2013ncbi.nlm.nih.gov
Fibrodysplasia ossificans progressiva (FOP) is a rare hereditary connective tissue disease
characterized by the progressive ectopic ossification of ligaments, tendons, and facial and
skeletal muscles throughout life. Symptoms begin in childhood as localized soft tissue
swellings. Immobility and articular dysfunction appear with involvement of the spine and
proximal extremities. The temporomandibular joint (TMJ) is a critical component involved in
the maxillofacial region, resulting in severe limitation of masticatory function, although TMJ …
Abstract
Fibrodysplasia ossificans progressiva (FOP) is a rare hereditary connective tissue disease characterized by the progressive ectopic ossification of ligaments, tendons, and facial and skeletal muscles throughout life. Symptoms begin in childhood as localized soft tissue swellings. Immobility and articular dysfunction appear with involvement of the spine and proximal extremities. The temporomandibular joint (TMJ) is a critical component involved in the maxillofacial region, resulting in severe limitation of masticatory function, although TMJ involvement is rare. The aim of this article is to present a 28-year-old man with dental problems and slowly progressive limitation of motion in the jaw, knees, shoulders and hips as well as neck distortion.
ncbi.nlm.nih.gov