Based upon case reports and small case series, it has been known for many years that
some types and subtypes of inherited epidermolysis bullosa (EB) may be at risk for
developing one or more extracutaneous complications. Many of these are associated with
considerable morbidity; some may result in death. Only over the past few years have there
been data generated from large, well characterized cohorts. However, these data, to date,
have been published almost exclusively in the nondermatologic literature. Our objective is to …