Cerebral vasculitis in X-linked lymphoproliferative disease cured by matched unrelated cord blood transplant

PE Gray, TA O'Brien, M Wagle, SG Tangye… - Journal of Clinical …, 2015 - Springer
PE Gray, TA O'Brien, M Wagle, SG Tangye, U Palendira, T Roscioli, S Choo, R Sutton…
Journal of Clinical Immunology, 2015Springer
Conclusion This is the second published description of joint disease in XLP, and only the
fourth case of non-EBV associated cerebral vasculitis in XLP, as well as being the first to be
successfully treated for this manifestation. This case raises specific questions about
vasculitis in XLP, in particular the potential relevance of HHV-7 to the pathogenesis.
Conclusion
This is the second published description of joint disease in XLP, and only the fourth case of non-EBV associated cerebral vasculitis in XLP, as well as being the first to be successfully treated for this manifestation. This case raises specific questions about vasculitis in XLP, in particular the potential relevance of HHV-7 to the pathogenesis.
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