Liver disease in cystic fibrosis
L Leeuwen, DA Fitzgerald, KJ Gaskin - Paediatric respiratory reviews, 2014 - Elsevier
The survival of patients with cystic fibrosis (CF) has progressively increased over recent
decades, largely attributable to early diagnosis through newborn screening and advances in
nutritional and respiratory care. As the life expectancy of patients with CF has improved, non-
respiratory complications such as liver disease have become increasingly recognized.
Biochemical derangements of liver enzymes in CF are common and may be attributed to a
number of specific hepatobiliary abnormalities. Among them, Cystic Fibrosis-associated …
decades, largely attributable to early diagnosis through newborn screening and advances in
nutritional and respiratory care. As the life expectancy of patients with CF has improved, non-
respiratory complications such as liver disease have become increasingly recognized.
Biochemical derangements of liver enzymes in CF are common and may be attributed to a
number of specific hepatobiliary abnormalities. Among them, Cystic Fibrosis-associated …
