Development, reliability, and validity of a novel Epidermolysis Bullosa Disease Activity and Scarring Index (EBDASI)
CCH Loh, J Kim, JC Su, BS Daniel… - Journal of the American …, 2014 - Elsevier
Background There is a lack of validated standardized outcome measures for epidermolysis
bullosa (EB) that can separate activity from damage. Objective We sought to develop and
validate an instrument for inherited EB of all ages and subtypes, the EB Disease Activity and
Scarring Index (EBDASI), which scores activity responsive to therapy separately from
scarring. Methods The EBDASI was validated by comparing its reliability and validity against
the Birmingham EB Severity (BEBS) score (partially validated with activity mixed with …
bullosa (EB) that can separate activity from damage. Objective We sought to develop and
validate an instrument for inherited EB of all ages and subtypes, the EB Disease Activity and
Scarring Index (EBDASI), which scores activity responsive to therapy separately from
scarring. Methods The EBDASI was validated by comparing its reliability and validity against
the Birmingham EB Severity (BEBS) score (partially validated with activity mixed with …
